I-cell disease

• almost all of the hydrolytic enzymes are missing from the lysosomes of many cell types.

• mis-sorting has been traced to a defective or missing GlcNAc phosphotransferase.

TLS Online TPP Program

#Id: 8090

#Section 2: General Biology

In triacylglycerols, glycerophospholipids, galactolipids, and sulfolipids, the alkyl groups are fatty acids in ester linkage. 

TLS Online TPP Program

#Id: 8089

#Section 2: General Biology

Beeswax is Triacontanoylpalmitate, is an ester of palmitic acid with the alcohol triacontanol.

TLS Online TPP Program

#Id: 8088

#Section 2: General Biology

The presence of one or more fatty acids with cis double bonds interferes with this tight packing and results in less stable aggregates.

TLS Online TPP Program

#Id: 8087

#Section 2: General Biology

Saturation = extent of packing

Fully saturated fatty acids in the extended form pack into nearly crystalline arrays, stabilized by many hydrophobic interactions.

TLS Online TPP Program

#Id: 8086

#Section 2: General Biology

TLS Online TPP Program

#Id: 8085

#Section 2: General Biology